Dermatofibrosarcoma

A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.

Also Known As:

Bednar Tumor; Bednar's Tumor; DFSP, Fibrosarcomatous; DFSP, Juvenile; DFSP, Myxoid; DFSP, Pigmented; Darier-Ferrand Tumor; Darier-Hoffmann Tumor; Dermatofibrosarcoma Protuberan; Dermatofibrosarcoma Protuberans, Familial; Dermatofibrosarcoma Protuberans, Fibrosarcomatous; Dermatofibrosarcoma Protuberans, Giant Cell; Dermatofibrosarcoma Protuberans, Myxoid; Dermatofibrosarcoma Protuberans, Pigmented; FS-DFSP; Familial Dermatofibrosarcoma Protuberans; Fibrosarcomatous Dermatofibrosarcoma Protuberans; Giant Cell Fibroblastoma; Giant Dermatofibrosarcoma Protuberans; Metastatic Dermatofibrosarcoma Protuberans; Bednars Tumor; Cell Fibroblastoma, Giant; Cell Fibroblastomas, Giant; DFSPs, Fibrosarcomatous; DFSPs, Juvenile; DFSPs, Myxoid; DFSPs, Pigmented; Darier Ferrand Tumor; Darier Hoffmann Tumor; Dermatofibrosarcoma Protuberan, Familial; Dermatofibrosarcoma Protuberan, Fibrosarcomatous; Dermatofibrosarcoma Protuberan, Giant; Dermatofibrosarcoma Protuberan, Metastatic; Dermatofibrosarcoma Protuberan, Myxoid; Dermatofibrosarcoma Protuberan, Pigmented; Dermatofibrosarcoma Protuberans; Dermatofibrosarcoma Protuberans, Giant; Dermatofibrosarcoma Protuberans, Metastatic; Dermatofibrosarcomas; Familial Dermatofibrosarcoma Protuberan; Fibroblastoma, Giant Cell; Fibroblastomas, Giant Cell; Fibrosarcomatous DFSP; Fibrosarcomatous DFSPs; Fibrosarcomatous Dermatofibrosarcoma Protuberan; Giant Cell Fibroblastomas; Giant Dermatofibrosarcoma Protuberan; Juvenile DFSP; Juvenile DFSPs; Metastatic Dermatofibrosarcoma Protuberan; Myxoid DFSP; Myxoid DFSPs; Myxoid Dermatofibrosarcoma Protuberan; Myxoid Dermatofibrosarcoma Protuberans; Pigmented DFSP; Pigmented DFSPs; Pigmented Dermatofibrosarcoma Protuberan; Pigmented Dermatofibrosarcoma Protuberans; Protuberan, Dermatofibrosarcoma; Protuberan, Familial Dermatofibrosarcoma; Protuberan, Fibrosarcomatous Dermatofibrosarcoma; Protuberan, Giant Dermatofibrosarcoma; Protuberan, Metastatic Dermatofibrosarcoma; Protuberan, Myxoid Dermatofibrosarcoma; Protuberan, Pigmented Dermatofibrosarcoma; Protuberans, Dermatofibrosarcoma; Protuberans, Familial Dermatofibrosarcoma; Protuberans, Fibrosarcomatous Dermatofibrosarcoma; Protuberans, Giant Dermatofibrosarcoma; Protuberans, Metastatic Dermatofibrosarcoma; Protuberans, Myxoid Dermatofibrosarcoma; Protuberans, Pigmented Dermatofibrosarcoma; Tumor, Bednar; Tumor, Bednar's; Tumor, Darier-Ferrand; Tumor, Darier-Hoffmann

Neoplasms: 1324753
- Neoplasms by Histologic Type: 2
  - Connective and Soft Tissue Neoplasms: 1
    - Sarcoma: 23140
      - Fibrosarcoma: 5536
        Dermatofibrosarcoma: 548
    - Connective Tissue Neoplasms: 9
      - Fibrous Tissue Neoplasms
        Fibrosarcoma: 5536
        Dermatofibrosarcoma: 548

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